Cutaneous mucinosis in mixed connective tissue disease ncbi. Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most reports deal with single cases or small series. Reticular erythematous mucinosis is a rare syndrome which can be misdiagnosed as seborrhoeic dermatitis. Papulonodular mucinosis in systemic lupus erythematosus. Examination of biopsy specimen showed focal mucin deposition in papillary and upper reticular dermis. Llinear morphea with secondary mucinosisinear morphea with. On alcian blue periodic acid schiff stain, abundant mucin deposition was demonstrated in the upper reticular dermis figure 3b. Reticular erythematous mucinosis the doctors doctor. Dermis sindrome rem o mucinosis reticular eritematosa. A repeat skin biopsy performed at our institute showed epidermal atrophy, hyalinization of collagen throughout the dermis and mucin deposition in upper reticular dermis figure 3a.
Pdf reticular erythematous mucinosis on the midline of the back. Reticular erythematous mucinosis primary care dermatology. Mucinosis eritematosa reticular reticular erythematous mucinosis. There are 0 terms under the parent term reticular erythematous mucinosis in the icd10cm alphabetical index. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most. Reticular erythematous mucinosis the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes.
Although the exact etiology remains undefined, efforts to. Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back. It is caused by mucinous infiltration of tissues, and usually involves the scalp, face, and neck. It is a disease that tends to affect women in the third and fourth decades of life. Jul 12, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Mucinous disorders of the skinbeyond the dermal mucinosis. Llinear morphea with secondary mucinosisinear morphea. Includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Reticular erythematous mucinosis on the midline of the back article pdf available in cutis. Reticular erythematous mucinosis and lupus erythematosus. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Courtesy of bryan anderson, md rarely, rem may occur on the extremities, head, neck, or groin, and there has been a single report of gingival involvement in a patient with typical lesions on the chest.
Reticular erythematous mucinosis rem is a disorder of dermal mucin accumulation that has been reported throughout the world. Benign or noncancerous forms of follicular mucinosis benign, primary or idiopathic follicular mucinosis are often of unknown cause. Multiple lesions may indicate the carney complex in which the benign tumours may develop in the. Induction of the disease has been associated with viral processes, solar irradiation, specific.
Suarezamor and others published mucinosis eritematosa reticular. Follicular mucinosis definition of follicular mucinosis by. The area is photosensitive and has been present for 1 year without resolution and without new lesions. Reticular erythematous mucinosis rem syndrome is a rare cutaneous disease first described by steigleder et al 1 more than 30 years ago. Reticular erythematous mucinosis rem is a rare chronic dermatosis that is typically characterized by reticular macular erythema or erythematous papules and plaques on the central area of the chest and back of middleaged women. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective. Department of dermatology, national defense medical college, 32 namiki, tokorozawa, saitama 35985, japan. Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides. Reticular erythematous mucinosis young to middle aged people women erythematous reticular or plaquelike eruption in the middle of the chest or back photoinduction. Aug 01, 2011 includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Predominantly affecting middleaged women, rem syndrome skin lesions are typically located on the central area of the chest or on the upper back but may also spread to the upper abdomen. Benign or noncancerous forms of follicular mucinosis benign, primary or. Sometimes follicular mucinosis may show up in skin biopsy results for other inflammatory skin diseases. Cutaneous mucinosis covers a heterogeneous group of diseases involving a diffuse and or focal mucin accumulation in the skin and its annexes.
Dermis mucinose eritematosa reticulada information on the. These findings point to the diagnosis of reticular mucinosis. Focal cutaneous mucinosis see the pathology of focal cutaneous mucinosis. Aug 01, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Is there a home remedy for reticular erythematous mucinosis.
Mar 26, 2010 is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Reticular erythematous mucinosis definition of reticular. Reticular erythematous mucinosis, journal of the european. At present, almost 100 patients with rem syndrome have been described. Reticular erythematous mucinosis rem syndrome is a rare, chronic disease characterized by asymptomatic, persistent reticular, slightly infiltrated erythematous plaques on chest andor back with slight infiltration. These are the first cases of mucinosis described in mixed connective tissue disease. Induction of the disease has been associated with viral processes, solar irradiation. These are most commonly seen on the chest and upper back.
Reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Clinical features and efficacy of antimalarial treatment for. Reticular erythematous mucinosis syndrome rem syndrome. By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them. Learn more about reticular erythematous mucinosis from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Cutaneous focal mucinosis is a skin condition characterized by a solitary nodule or papule 189. Papulonodular mucinosis in systemic lupus erythematosus victoria g ortiz md a, ravi s krishnan md a, ling l chen md b, and sylvia hsu md a dermatology online journal 10 2. The leading primary care society for dermatology and skin surgery.
Icd10cm alphabetical index reticular erythematous mucinosis. It presents with reticular, macular lesions or erythematous papules and plaques. Jan 11, 2019 reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Cutaneous mucinosis in mixed connective tissue disease. Reticular erythematous mucinosis is a chronic and rare syndrome of. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective treatment modalities have been encouraging. She has been on topical and oral steroids without resolution. Mucinosis eritematosa reticular actas dermosifiliograficas. It is also called midline mucinosis or plaquelike cutaneous mucinosis. The cutaneous mucinoses are a heterogeneous group of diseases in which mucin accumulates in the skin or within the hair follicle. Reticular erythematous mucinosis rem, rem syndrome. Pdf sindrome rem associada a lupus eritematoso sistemico e. Treatment of reticular erythematous mucinosis with uva1. Mucinosis eritematosa reticular actas dermosifiliogr 2004.